Karatas, ZehraKaraarslan, SevimAlp, HayrullahSarigul, AliBaysal, Tamer2024-02-232024-02-2320131301-5680https://doi.org/10.5606/tgkdc.dergisi.2013.6137https://hdl.handle.net/20.500.12452/17049Hennekam syndrome is an autosomal recessive disorder, characterized by lymphangiectasia in internal organs with lymphedema. Pleural or pericardial effusions may present with lymphedema on extremities in the course of the disease. Although a poor long-chain fatty diet is given for treatment, its success rate is low. In this article, we report the results of a successful pericardiectomy performed on a 21-month-old boy who was diagnosed with Hennekam syndrome.trinfo:eu-repo/semantics/closedAccessHennekam SyndromePericardial EffusionPericardiectomyArticle214111011132-s2.0-84889576024Q3WOS:000326410100048Q410.5606/tgkdc.dergisi.2013.6137