Successful pericardiectomy in Hennekam syndrome

dc.contributor.authorKaratas, Zehra
dc.contributor.authorKaraarslan, Sevim
dc.contributor.authorAlp, Hayrullah
dc.contributor.authorSarigul, Ali
dc.contributor.authorBaysal, Tamer
dc.date.accessioned2024-02-23T14:44:40Z
dc.date.available2024-02-23T14:44:40Z
dc.date.issued2013
dc.departmentNEÜen_US
dc.description.abstractHennekam syndrome is an autosomal recessive disorder, characterized by lymphangiectasia in internal organs with lymphedema. Pleural or pericardial effusions may present with lymphedema on extremities in the course of the disease. Although a poor long-chain fatty diet is given for treatment, its success rate is low. In this article, we report the results of a successful pericardiectomy performed on a 21-month-old boy who was diagnosed with Hennekam syndrome.en_US
dc.identifier.doi10.5606/tgkdc.dergisi.2013.6137
dc.identifier.endpage1113en_US
dc.identifier.issn1301-5680
dc.identifier.issue4en_US
dc.identifier.scopus2-s2.0-84889576024en_US
dc.identifier.scopusqualityQ3en_US
dc.identifier.startpage1110en_US
dc.identifier.urihttps://doi.org/10.5606/tgkdc.dergisi.2013.6137
dc.identifier.urihttps://hdl.handle.net/20.500.12452/17049
dc.identifier.volume21en_US
dc.identifier.wosWOS:000326410100048en_US
dc.identifier.wosqualityQ4en_US
dc.indekslendigikaynakWeb of Scienceen_US
dc.indekslendigikaynakScopusen_US
dc.language.isotren_US
dc.publisherBaycinar Medical Publ-Baycinar Tibbi Yayinciliken_US
dc.relation.ispartofTurk Gogus Kalp Damar Cerrahisi Dergisi-Turkish Journal Of Thoracic And Cardiovascular Surgeryen_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/closedAccessen_US
dc.subjectHennekam Syndromeen_US
dc.subjectPericardial Effusionen_US
dc.subjectPericardiectomyen_US
dc.titleSuccessful pericardiectomy in Hennekam syndromeen_US
dc.typeArticleen_US

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